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oculoauricular dysplasiaoculoauriculovertebral (OAV) dysplasia
a congenital condition in which colobomas of the upper eyelid, epibulbar dermoids, bilateral accessory auricular appendages
anterior to the ears, and vertebral anomalies are frequently associated with characteristic facies, consisting of asymmetry
of the skull, prominent frontal bossing, low hairline, mandibular hypoplasia, low-set ears, and sometimes hemifacial microstomia.
Called also Goldenhar syndrome, mandibulofacial dysostosis with epibulbar dermoids, and OAV syndrome.

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